nefrНефрологияNephrology (Saint-Petersburg)1561-62742541-9439Pavlov First Saint-Petersburg State Medical University10.24884/1561-6274-2010-14-2-78-84nefr-1222Research ArticleПРОГРАММА НЕПРЕРЫВНОГО ПОСЛЕДИПЛОМНОГО ОБРАЗОВАНИЯ ПО НЕФРОЛОГИИPROGRAM ON CONTINUOUS POSTGRADUATE EDUCATION ON NEPHROLOGYПЕРВИЧНАЯ ИНТЕСТИНАЛЬНАЯ ЛИМФАНГИЭКТАЗИЯ (болезнь Вальдманна)PRIMARY INTESTINAL LYMPHANGIECTASIA (Waldmann disease)СмирновА. В.SmirnovA. V.

кафедра пропедевтики внутренних болезней,

Научно-исследовательский институт нефрологии.

ВиноградоваТ. В.VinogradovaT. V.

кафедра пропедевтики внутренних болезней.

197022, Санкт-Петербург, ул. Толстого, д.17, СПбГМУ им. акад. И.П. Павлова, нефрокорпус, тел. (812) 234­-91-94.

kaukov@nephrolog.ruВоронковаЕ. В.VoronkovaE. V.

кафедра пропедевтики внутренних болезней.

КаюковИ. Г.KayukovI. G.

Научно-исследовательский институт нефрологии,

кафедра нефрологии и диализа.

НутфуллинаГ. М.NutfullinaG. M.

кафедра патологической анатомии.

ТрофименкоИ. И.TrofimenkoI. I.

кафедра пропедевтики внутренних болезней.

ШумилинаА. А.ShumilinaA. A.

кафедра пропедевтики внутренних болезней.

Санкт-Петербургский государственный медицинский университет им. акад. И.П. ПавловаRussian Federation2010100220101427884Copyright © Смирнов А.В., Виноградова Т.В., Воронкова Е.В., Каюков И.Г., Нутфуллина Г.М., Трофименко И.И., Шумилина А.А., 20102010Смирнов А.В., Виноградова Т.В., Воронкова Е.В., Каюков И.Г., Нутфуллина Г.М., Трофименко И.И., Шумилина А.А.Smirnov A.V., Vinogradova T.V., Voronkova E.V., Kayukov I.G., Nutfullina G.M., Trofimenko I.I., Shumilina A.A.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://journal.nephrolog.ru/jour/article/view/1222

Приводится описание редкого заболевания первичной интестинальной лимфангиоэктазии – болезни Вальдманна. Клиника заболевания представлена выраженными отеками нижних конечностей, сочетающимися с дилатацией лимфатических сосудов тонкого кишечника и развитием на этом фоне энтеропатии с полидефицитным состоянием (гипопротеинемия, гипоглобулинемия, снижение уровня жирорастворимых витаминов 25(ОН)D₃, фолиевой кислоты). Этиология и патогенез заболевания в настоящее время не изучены.

The description of a rare disease of primary intestinal lymphangiectasia – Waldmann disease is discussed. The clinic of disease is presented by edema of the lower course limbs combined with dilatation of lymphaic vessels of small intestine and development on this background of enteropathy with polideficiency state (hypoproteinemia, hypoglobulinemiya, reduction of fat-soluble vitamins 25(OH)D₃, folic acid). Etiology and pathogenesis of the disease is not currently understood.

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The authors declare that there are no conflicts of interest present.