nefrНефрологияNephrology (Saint-Petersburg)1561-62742541-9439Pavlov First Saint-Petersburg State Medical University10.24884/1561-6274-2013-17-5-89-95nefr-447Research ArticleНАБЛЮДЕНИЯ ИЗ ПРАКТИКИPRACTICAL NOTESМНОЖЕСТВЕННЫЙ ЛИПОМАТОЗ (БОЛЕЗНЬ МАДЕЛУНГА) И ПОРАЖЕНИЕ ПОЧЕК. ДВА КЛИНИЧЕСКИХ СЛУЧАЯMULTIPLE LIPOMATOSIS (MADELUNG’S DISEASE) AND KIDNEY INJURY. TWO CLINICAL CASESБатюшинМ. М.BatyushinM. M.

Кафедра внутренних болезней с основами физиотерапии № 2

344022, г. Ростов-на-Дону, пер. Нахичеванский, д. 29, тел.: 8-918-501-88-01

batjushin-m@rambler.ruПасечникА. В.PasechnikA. V.

консультативная поликлиника

СадовничаяН. А.SadovnichayaN. A.

нефрологическое отделение

Ростовский государственный медицинский университет Министерства здравоохранения Российской ФедерацииRussian Federation2013100520131758995Copyright © Батюшин М.М., Пасечник А.В., Садовничая Н.А., 20132013Батюшин М.М., Пасечник А.В., Садовничая Н.А.Batyushin M.M., Pasechnik A.V., Sadovnichaya N.A.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://journal.nephrolog.ru/jour/article/view/447

В статье приводится обзор литературы по проблеме системного липоматоза (болезни Маделунга), а также два клинических описания системного липоматоза в сочетании с патологией почек. Оба пациента мужского пола. В первом случае наблюдалось сочетание липоматоза с микроскопическим полиангиитом и поражением почек по типу гломерулонефрита. Во втором случае липоматоз сочетался с хроническим гломерулонефритом, развившемся на фоне рака почки, и болезнью фон Гиппеля–Линдау.

This article provides an overview of the literature on systemic lipomatosis (Madelung's disease), as well as two clinical descriptions of the system lipomatosis in combination with kidney disease. Both male patient. In the first case, a combination with a microscopic poliangiit lipomatosis and renal injury on the type of glomerulonephritis. In the second case lipomatosis combined with chronic glomerulonephritis that developed against the background of renal cancer and disease von Hippel–Lindau.

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The authors declare that there are no conflicts of interest present.