nefrНефрологияNephrology (Saint-Petersburg)1561-62742541-9439Pavlov First Saint-Petersburg State Medical University10.24884/1561-6274-2013-17-3-88-92nefr-502Research ArticleНАБЛЮДЕНИЯ ИЗ ПРАКТИКИPRACTICAL NOTESДИСГЕНЕЗИЯ ПРОКСИМАЛЬНЫХ КАНАЛЬЦЕВ ПОЧКИ: СЛУЧАЙ ИЗ ПРАКТИКИ С БЛАГОПРИЯТНЫМ ИСХОДОМRENAL PROXIMAL TUBULES DISGENESIS: CASE HISTORY WITH SUCCESSFUL OUTCOMEСавошВ. В.SavoshV. V.

кафедра патологической анатомии

СукалоА. В.SukaloA. V.

1-я кафедра детских болезней

ЛетковскаяТ. А.LetkovskajaT. A.

кафедра патологической анатомии

КозыроИ. А.KozyroI. A.

220116, Минск, пр. Дзержинского, д. 83. 1-я кафедра детских болезней

Kozyroia@mail.ruТурН. И.TurN. I.Белорусский государственный медицинский университетBelarus2-я детская городская клиническая больницаBelarus2013100320131738892Copyright © Савош В.В., Сукало А.В., Летковская Т.А., Козыро И.А., Тур Н.И., 20132013Савош В.В., Сукало А.В., Летковская Т.А., Козыро И.А., Тур Н.И.Savosh V.V., Sukalo A.V., Letkovskaja T.A., Kozyro I.A., Tur N.I.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://journal.nephrolog.ru/jour/article/view/502

Авторы приводят описание случая диагностики врожденной дисгенезии проксимальных канальцев почки, явившейся причиной хронической почечной недостаточности у новорожденного ребенка. Диагноз морфологически верифицирован в возрасте 11 дней, включая иммуногистохимическое исследование нефробиоптата с антителами к эпителиальному мембранному антигену. С 3-дневного возраста было налажено проведение автоматического перитонеального диализа и сеансов вено-венозной гемофильтрации с последующей успешной трансплантацией почки (в возрасте 4,1 года).

Authors describe a case of diagnostic of proximal renal tubules congenital dysgenesis leaded to chronic kidney disease in newborn. Diagnosis was morphologically proved at the age of 11 days, including immunohistochemical study of kidney biopsy specimen with monoclonal antibodies to epithelial membrane antigen. Automatic peritoneal dialysis and veno-venous hemofiltration were started at the age of 3 days with positive effect. The successful kidney transplantation was done in 4,1 years old child.

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The authors declare that there are no conflicts of interest present.