nefrНефрологияNephrology (Saint-Petersburg)1561-62742541-9439Pavlov First Saint-Petersburg State Medical Universitynefr-91Research ArticleНАБЛЮДЕНИЯ ИЗ ПРАКТИКИPRACTICAL NOTESОсобенности течения и лечения «акушерского» атипичного гемолитико-уремического синдрома (аГУС)Course and treatment characteristics of “obstetric” atypical hemolytic-uremic syndrome (aHUS)КоротчаеваЮ. В.KorotchaevaY. V.lumis-j@bk.ruКозловскаяН. Л.KozlovskayaN. L.noemail@neicon.ruБондаренкоТ. В.BondarenkoT. V.noemail@neicon.ruВеселовГ. А.VeselovG. A.noemail@neicon.ruПервый Московский государственный медицинский университет им. И.М. СеченоваРоссияI.M.Sechenov First Moscow State Medical UniversityRussian FederationГородская клиническая больница им. А.К. ЕрамишанцеваРоссияClinical city hospital named A.K. EramishantcevaRussian Federation2015010320151927681Copyright © Коротчаева Ю.В., Козловская Н.Л., Бондаренко Т.В., Веселов Г.А., 20152015Коротчаева Ю.В., Козловская Н.Л., Бондаренко Т.В., Веселов Г.А.Korotchaeva Y.V., Kozlovskaya N.L., Bondarenko T.V., Veselov G.A.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://journal.nephrolog.ru/jour/article/view/91

Приводится наблюдение атипичного гемолитико-уремического синдрома (аГУС), развившегося в конце II триместра беременности и проявившегося тяжелой полиорганной патологией, включая поражение почек, сердца, легких, нервной системы и плаценты. В результате ранней диагностики и своевременно начатой экстракорпоральной терапии в сочетании с низкомолекулярными гепаринами (НМГ) острая тромботическая микроангиопатия (ТМА) купирована с полным восстановлением функции всех поврежденных органов.

It is presented the case of rare aHUS that developed late in the second trimester of pregnancy, and showed severe multiple organ pathology, including the kidneys, heart, lungs, nervous system and placenta. As a result, early diagnosis and timely plazmotherapy started in conjunction with LMWH acute TMA eliminated with full restoration of function of damaged organs.

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The authors declare that there are no conflicts of interest present.