BARTTER SYNDROME IN CHILDREN
https://doi.org/10.24884/1561-6274-2012-16-3/2-25-33
Abstract
This review is a generalisation of modern conceptions about Bartter Syndrome – autosomal-recessive tubulopathy with impairment of K, Na, Cl transport system in distal tubule in the thick ascending limb of Henle’s loop. Data about K, Na, Cl transport regulation mechanisms, pathogenic and clinical features are generalized. The diagnostic algorithms and approachs to the treatment of Bartter Syndrom in children are presented.
About the Authors
J. G. Leviashvili
Санкт-Петербурская педиатрическая медицинская академия
Russian Federation
Russian Federation
N. D. Savenkova
Санкт-Петербурская педиатрическая медицинская академия
Russian Federation
Russian Federation
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Review
For citations:
Leviashvili J.G., Savenkova N.D. BARTTER SYNDROME IN CHILDREN. Nephrology (Saint-Petersburg). 2012;16(3/2):25-33. (In Russ.) https://doi.org/10.24884/1561-6274-2012-16-3/2-25-33
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