RENAL PATHOLOGY FEATURES IN CHILDREN WITH LOWE SYNDROME
Abstract
The features of renal pathology in the oculo-cerebro-renal Lowe syndrome (OCRL) in children. Renal pathology is characterized by tubulopathy with generalized defect of glucose transport systems, amino acids, phosphates, bicarbonates in proximal tubules, manifested syndrome Fanconi, rarely combined with congenital ureterohydronephrosis, proteinuria, incomplete nephrotic syndrome.
About the Authors
J. G. Leviashvili
Saint-Petersburg state pediatric medical university
Russian Federation
Russian Federation
N. D. Savenkova
Saint-Petersburg state pediatric medical university
Russian Federation
Russian Federation
I. V. Anichkova
Saint-Petersburg state pediatric medical university
Russian Federation
Russian Federation
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Review
For citations:
Leviashvili J.G., Savenkova N.D., Anichkova I.V. RENAL PATHOLOGY FEATURES IN CHILDREN WITH LOWE SYNDROME. Nephrology (Saint-Petersburg). 2015;19(6):53-60. (In Russ.)
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