БАРТТЕР СИНДРОМ У ДЕТЕЙ
https://doi.org/10.24884/1561-6274-2012-16-3/2-25-33
Аннотация
Данный обзор является обобщением современных представлений о Барттер синдроме – тубулопатии с аутосомнорецессивным типом наследования, нарушением систем транспорта К, Na, Cl в дистальном канальце в толстом восходящем колене петли Генле. Обобщены данные о механизмах регуляции транспорта К, Na, Cl, патогенетических и клинических особенностях, рассмотрены диагностические алгоритмы, подходы к терапии Барттер синдрома у детей.
Об авторах
Ж. Г. Левиашвили
Санкт-Петербурская педиатрическая медицинская академия
Россия
Россия
Кафедра факультетской педиатрии
1941000, Санкт-Петербург, ул. Литовская, д. 2. Тел. 952-98-09
Н. Д. Савенкова
Санкт-Петербурская педиатрическая медицинская академия
Россия
Кафедра факультетской педиатрии
Россия
Кафедра факультетской педиатрии
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Рецензия
Для цитирования:
Левиашвили Ж.Г., Савенкова Н.Д. БАРТТЕР СИНДРОМ У ДЕТЕЙ. Нефрология. 2012;16(3/2):25-33. https://doi.org/10.24884/1561-6274-2012-16-3/2-25-33
For citation:
Leviashvili J.G., Savenkova N.D. BARTTER SYNDROME IN CHILDREN. Nephrology (Saint-Petersburg). 2012;16(3/2):25-33. (In Russ.) https://doi.org/10.24884/1561-6274-2012-16-3/2-25-33
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