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БАРТТЕР СИНДРОМ У ДЕТЕЙ

https://doi.org/10.24884/1561-6274-2012-16-3/2-25-33

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Аннотация

Данный обзор является обобщением современных представлений о Барттер синдроме – тубулопатии с аутосомнорецессивным типом наследования, нарушением систем транспорта К, Na, Cl в дистальном канальце в толстом восходящем колене петли Генле. Обобщены данные о механизмах регуляции транспорта К, Na, Cl, патогенетических и клинических особенностях, рассмотрены диагностические алгоритмы, подходы к терапии Барттер синдрома у детей.

Об авторах

Ж. Г. Левиашвили
Санкт-Петербурская педиатрическая медицинская академия
Россия

Кафедра факультетской педиатрии 

1941000, Санкт-Петербург, ул. Литовская, д. 2. Тел. 952-98-09



Н. Д. Савенкова
Санкт-Петербурская педиатрическая медицинская академия
Россия
Кафедра факультетской педиатрии


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Рецензия

Для цитирования:


Левиашвили Ж.Г., Савенкова Н.Д. БАРТТЕР СИНДРОМ У ДЕТЕЙ. Нефрология. 2012;16(3/2):25-33. https://doi.org/10.24884/1561-6274-2012-16-3/2-25-33

For citation:


Leviashvili J.G., Savenkova N.D. BARTTER SYNDROME IN CHILDREN. Nephrology (Saint-Petersburg). 2012;16(3/2):25-33. (In Russ.) https://doi.org/10.24884/1561-6274-2012-16-3/2-25-33

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ISSN 1561-6274 (Print)
ISSN 2541-9439 (Online)