PRIMARY INTESTINAL LYMPHANGIECTASIA (Waldmann disease)
https://doi.org/10.24884/1561-6274-2010-14-2-78-84
Abstract
The description of a rare disease of primary intestinal lymphangiectasia – Waldmann disease is discussed. The clinic of disease is presented by edema of the lower course limbs combined with dilatation of lymphaic vessels of small intestine and development on this background of enteropathy with polideficiency state (hypoproteinemia, hypoglobulinemiya, reduction of fat-soluble vitamins 25(OH)D₃, folic acid). Etiology and pathogenesis of the disease is not currently understood.
About the Authors
A. V. Smirnov
Санкт-Петербургский государственный медицинский университет им. акад. И.П. Павлова
Russian Federation
Russian Federation
T. V. Vinogradova
Санкт-Петербургский государственный медицинский университет им. акад. И.П. Павлова
Russian Federation
Russian Federation
E. V. Voronkova
Санкт-Петербургский государственный медицинский университет им. акад. И.П. Павлова
Russian Federation
Russian Federation
I. G. Kayukov
Санкт-Петербургский государственный медицинский университет им. акад. И.П. Павлова
Russian Federation
Russian Federation
G. M. Nutfullina
Санкт-Петербургский государственный медицинский университет им. акад. И.П. Павлова
Russian Federation
Russian Federation
I. I. Trofimenko
Санкт-Петербургский государственный медицинский университет им. акад. И.П. Павлова
Russian Federation
Russian Federation
A. A. Shumilina
Санкт-Петербургский государственный медицинский университет им. акад. И.П. Павлова
Russian Federation
Russian Federation
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Review
For citations:
Smirnov A.V., Vinogradova T.V., Voronkova E.V., Kayukov I.G., Nutfullina G.M., Trofimenko I.I., Shumilina A.A. PRIMARY INTESTINAL LYMPHANGIECTASIA (Waldmann disease). Nephrology (Saint-Petersburg). 2010;14(2):78-84. (In Russ.) https://doi.org/10.24884/1561-6274-2010-14-2-78-84
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